Cardiac Anomalies in Dandy-Walker Syndrome

Prevalence and Diagnosis

• The American Academy of Pediatrics recommends that cardiac evaluation is essential at diagnosis of Dandy-Walker syndrome, as cardiac defects occur in approximately 40% of cases 1

Clinical Management Implications

• The American Heart Association suggests that all infants diagnosed with Dandy-Walker syndrome require comprehensive cardiac evaluation at the time of diagnosis, including physical examination with specific attention to cardiac findings 1